R2 Merritt, Alexander

Alex Merritt

Hi Alex

For the sake of time I think we should just do heart/hands in collagen vascular disease – SLE, Scleroderma and RA

You should be able to stay on this page and present it all from here

  • The way it is organized
    • Disease name
    • Heart disease with frequent components bolded
    • Hands – an image of the hands in the disease
Our Patient

65 year old female with longstanding history of SLE, Lupus Sjogren’s and Raynaud’s

JACCOUD’S ARTHROPATHY
65 year old female with longstanding history of SLE, Lupus Sjogren’s and Raynaud’s  Xray shows non erosive arthropathy with ulnar deviation of 2nd through 5th MCP joints

SLE
Heart
  • Pancarditis
    •  pericardium, pericarditis 25% most common
    • myocardium, myocarditis is rare and caused by vasculitis
    • endocardium – Libman-Sacks 10%  mitral and tricuspid valve
  • myocardial infarction 9X increase
  • Cardiac complications in  about 50% and major cause of death

SLE and the Heart TCV

Scleroderma
  • Heart
    • Pulmonary hypertension secondary to lung and renal disease
      • right sided disease – increase RV and RA
    • Pancarditis
      • pericardial disease
      • myocardial disease, – myocardial fibrosis
      • conduction system abnormalities, arrhythmias,
      • Endocardium and valvular disease – infrequent

  • Scleroderma,  Pulmonary Hypertension RVF Cor Pulmonale Pericardial effusion 
    40 year old female with known interstitial lung disease (a and b) shows enlarged right atrium and right ventricle and small pericardial effusion (c and overlaid in maroon in d) and enlarged esophagus (overlay in pink in d) and an edematous gallbladder wall from chronic right heart failure.
Hands

Soft Tissue Calcification Ulnar Deviation

SCLERODERMA
Radiographs of both hands show abnormal alignment of the metacarpophalangeal joints, most marked on the left, in keeping with subluxation. The bone density appears normal. There is joint space loss and evidence of erosive arthropathy particularly evident at the metacarpophalangeal joinft of the right 3rd and 4th MCP’s. Dense soft tissue calcifications are seen in the fingertips and along the ulnar aspect of the right wrist/distal forearm.
Case courtesy of Dr Jan Frank Gerstenmaier,
Radiopaedia.org, rID: 23125

Acroosteolysis

SCLERODERMA
Acroosteolysis in a female patient with scleroderma
Case courtesy of Dr Minh Xuan Truong,
Radiopaedia

 

TCV –Scleroderma and the Heart

Rheumatoid Arthritis
Heart
  • Increased incidence of
    • congestive heart failure and
    • ischemic heart disease associated with an
    • increased mortality
  • Pancarditis
Hands

Erosive Osteoarthritis dominant in the MCPs and Carpals

RHEUMATOID ARTHRITIS
Showing degenerative and erosive changes dominantly at the MCP joints, intercarpal joints, ulnar carpal and radiocarpal joints and to lesser extent the PIP joints. There is ulnar deviation more prominent on the right hand
Ashley Davidoff MD

Rheumatoid Arthritis and Heart Disease TCV
RA and the Hand TCV

For more extensive info in see TCV on Hands and Heart 

Next  Marc Salomon,   65 F with fatigue and dyspnea